Dual Outlet Right Ventricle (DORV) status post Fontan as palliation for common atrioventricular canal defect causing functional single ventricle heart disease
Other features include:
- Interrupted inferior vena cava (IVC) with azygus continuation to the left superior vena cava (SVC),
- Bilateral SVCs
- ligated native pulmonary artery (PA)
- heterotaxy